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Actions	Set of 11 clinical photographs and x-rays documenting a case of Cleidocranial dysostosis Remove from selection Add to selection Object numberED.CS.2022.54 TitleSet of 11 clinical photographs and x-rays documenting a case of Cleidocranial dysostosis DescriptionSet of 11 clinical photographs and x-rays documenting a case of Cleido-Cranial Dyostosis. Cleidocranial dysostosis CCD) 1. Skull - Brachycephalic with frontal, parietal and occipital prominance and wide depression, and persistence of the anterior fontanelle and of the metopic suture. Numerous Wormian bones are present in sutures of the vault (Figs. 1-7). 2. Face - Hypoplasia of the maxialla and of the mandible, but the growth in length of the latter is less disturbed and relative prognathism results (Figs. 1, 3, and 5). An associated delay in dentination occurs and the formation of dentin is poor leading to considerable dental decay. 3. Clavicles - Defective development, in varying degrees, of the clavicles, usually asymmetrically on the two sides and when extensive permitting abnormal approximation of the shoulders anteriory (Figs. 1, 2, 4, and 8). Defects of the pectoralis major muscles in extent proportionate to the clavicular defects. 4. Spine - Late fusion of the nueral arches. 5. Pelvis - Defective ossification of the pubic bones (the cartilaginous structure is present and palpable). Delayed ossification (shown by widening) of the regions of the sacro-iliac joints and the tridadiate cartilages of the acetabula (Fig. 11). 6. Some delay in growth in epiphyseal plates leading to a degree of stunting of growth. 7. Hands - A peripheral dysostosis with additional secondary ossific centres in the metacarples. Disproportionate enlargement of the epiphysis, for the terminal phalanx of the thumb and tapering of the tips of all the terminal phalanges. Selective distortion of the middle phalanx of the fifth finger with 'pegging' of its epiphysis (an appearance sometimes also found in achrondroplasia (Fig. 9). 8. Feet - These also show a peripheral dysostosis with 'pegging' of the epiphysis of the proximal phalanges and a marked disproportionate enlargement of the epiphysis of the terminal phalanx of the hallux and tapering of its extremeity (Fig. 10) Object nameBone and joint surgery Object categoryPatient Photography Dimensions Largest Width: 14.5 Height: 11

Object numberED.CS.2022.54

TitleSet of 11 clinical photographs and x-rays documenting a case of Cleidocranial dysostosis

DescriptionSet of 11 clinical photographs and x-rays documenting a case of Cleido-Cranial Dyostosis. Cleidocranial dysostosis CCD) 1. Skull - Brachycephalic with frontal, parietal and occipital prominance and wide depression, and persistence of the anterior fontanelle and of the metopic suture. Numerous Wormian bones are present in sutures of the vault (Figs. 1-7). 2. Face - Hypoplasia of the maxialla and of the mandible, but the growth in length of the latter is less disturbed and relative prognathism results (Figs. 1, 3, and 5). An associated delay in dentination occurs and the formation of dentin is poor leading to considerable dental decay. 3. Clavicles - Defective development, in varying degrees, of the clavicles, usually asymmetrically on the two sides and when extensive permitting abnormal approximation of the shoulders anteriory (Figs. 1, 2, 4, and 8). Defects of the pectoralis major muscles in extent proportionate to the clavicular defects. 4. Spine - Late fusion of the nueral arches. 5. Pelvis - Defective ossification of the pubic bones (the cartilaginous structure is present and palpable). Delayed ossification (shown by widening) of the regions of the sacro-iliac joints and the tridadiate cartilages of the acetabula (Fig. 11). 6. Some delay in growth in epiphyseal plates leading to a degree of stunting of growth. 7. Hands - A peripheral dysostosis with additional secondary ossific centres in the metacarples. Disproportionate enlargement of the epiphysis, for the terminal phalanx of the thumb and tapering of the tips of all the terminal phalanges. Selective distortion of the middle phalanx of the fifth finger with 'pegging' of its epiphysis (an appearance sometimes also found in achrondroplasia (Fig. 9). 8. Feet - These also show a peripheral dysostosis with 'pegging' of the epiphysis of the proximal phalanges and a marked disproportionate enlargement of the epiphysis of the terminal phalanx of the hallux and tapering of its extremeity (Fig. 10)

Object nameBone and joint surgery

Object categoryPatient Photography

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